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Case Reports

Porto pulmonary hypertension due to progression of secondary biliary cirrhosis following Kasai procedure

Authors:

R. C. Herath ,

Sri Jayewardenepura General Hospital, Colombo, LK
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K. V. Ruwanpura,

Sri Jayewardenepura General Hospital, Colombo, LK
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T. C. Prathapasinghe,

Sri Jayewardenepura General Hospital, Colombo, LK
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C. De Silva

Sri Jayewardenepura General Hospital, Colombo, LK
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Abstract

Porto pulmonary hypertension is the presence of pulmonary arterial hypertension in patients with advanced liver disease and portal hypertension. It affects minority of advanced liver disease patients without a significant correlation between hepatic impairment and severe porto pulmonary hypertension. It is a rare complication of portal hypertension following successful portoenterostomy. We present a case of a seventeen-year-old male with a past history of Kasai procedure for congenital biliary atresia, presenting with severe pulmonary hypertension as a complication of cirrhosis. He was defaulted during childhood follow up and was asymptomatic during last 17 years which has led to silent progression of secondary biliary cirrhosis. Hence this highlights the importance of long-termfollow up after Kasai procedure.
How to Cite: Herath, R.C., Ruwanpura, K.V., Prathapasinghe, T.C. and De Silva, C., 2021. Porto pulmonary hypertension due to progression of secondary biliary cirrhosis following Kasai procedure. Journal of the Ceylon College of Physicians, 52(2), pp.112–114. DOI: http://doi.org/10.4038/jccp.v52i2.7943
Published on 31 Dec 2021.
Peer Reviewed

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